Erdheim–Chester disease misdiagnosed as meningioma of the pontocerebellar angle: A case report and review of literature
Erdheim–Chester Disease (ECD) is a rare non-Langerhans form of systemic histiocytosis of unknown etiology with multiple organ involvement. It most commonly affects the long bones, lungs, heart, retroperitoneum, eyes, and kidneys and less commonly the brain and spinal cord. Although there are very fe...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2023-07-01
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| Series: | Indian Journal of Pathology and Microbiology |
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| Online Access: | https://journals.lww.com/10.4103/ijpm.ijpm_1121_21 |
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| author | Ali Riza Guvercin Beyhan Guvercin Emel Çakır Uğur Yazar |
| author_facet | Ali Riza Guvercin Beyhan Guvercin Emel Çakır Uğur Yazar |
| author_sort | Ali Riza Guvercin |
| collection | DOAJ |
| description | Erdheim–Chester Disease (ECD) is a rare non-Langerhans form of systemic histiocytosis of unknown etiology with multiple organ involvement. It most commonly affects the long bones, lungs, heart, retroperitoneum, eyes, and kidneys and less commonly the brain and spinal cord. Although there are very few cases of supratentorial ECD mimicking intracranial meningioma reported in literature, to the best of our knowledge, there are no reports on ECD mimicking infratentorial pontocerebellar angle meningioma. The present study reports a case of ECD mimicking pontocerebellar angle meningioma. This study aimed to emphasize the importance of systemic evaluation using a multidisciplinary approach as well as the need for considering ECD as a differential diagnosis of xanthomatous meningioma. |
| format | Article |
| id | doaj-art-30504335f99f433288b0788b613df41b |
| institution | Kabale University |
| issn | 0377-4929 |
| language | English |
| publishDate | 2023-07-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Journal of Pathology and Microbiology |
| spelling | doaj-art-30504335f99f433288b0788b613df41b2025-02-07T13:37:42ZengWolters Kluwer Medknow PublicationsIndian Journal of Pathology and Microbiology0377-49292023-07-0166364464710.4103/ijpm.ijpm_1121_21Erdheim–Chester disease misdiagnosed as meningioma of the pontocerebellar angle: A case report and review of literatureAli Riza GuvercinBeyhan GuvercinEmel ÇakırUğur YazarErdheim–Chester Disease (ECD) is a rare non-Langerhans form of systemic histiocytosis of unknown etiology with multiple organ involvement. It most commonly affects the long bones, lungs, heart, retroperitoneum, eyes, and kidneys and less commonly the brain and spinal cord. Although there are very few cases of supratentorial ECD mimicking intracranial meningioma reported in literature, to the best of our knowledge, there are no reports on ECD mimicking infratentorial pontocerebellar angle meningioma. The present study reports a case of ECD mimicking pontocerebellar angle meningioma. This study aimed to emphasize the importance of systemic evaluation using a multidisciplinary approach as well as the need for considering ECD as a differential diagnosis of xanthomatous meningioma.https://journals.lww.com/10.4103/ijpm.ijpm_1121_21erdheim–chester diseaseintracranialmmeningioma |
| spellingShingle | Ali Riza Guvercin Beyhan Guvercin Emel Çakır Uğur Yazar Erdheim–Chester disease misdiagnosed as meningioma of the pontocerebellar angle: A case report and review of literature Indian Journal of Pathology and Microbiology erdheim–chester disease intracranialm meningioma |
| title | Erdheim–Chester disease misdiagnosed as meningioma of the pontocerebellar angle: A case report and review of literature |
| title_full | Erdheim–Chester disease misdiagnosed as meningioma of the pontocerebellar angle: A case report and review of literature |
| title_fullStr | Erdheim–Chester disease misdiagnosed as meningioma of the pontocerebellar angle: A case report and review of literature |
| title_full_unstemmed | Erdheim–Chester disease misdiagnosed as meningioma of the pontocerebellar angle: A case report and review of literature |
| title_short | Erdheim–Chester disease misdiagnosed as meningioma of the pontocerebellar angle: A case report and review of literature |
| title_sort | erdheim chester disease misdiagnosed as meningioma of the pontocerebellar angle a case report and review of literature |
| topic | erdheim–chester disease intracranialm meningioma |
| url | https://journals.lww.com/10.4103/ijpm.ijpm_1121_21 |
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