Anomalous origin of a right pulmonary artery identified with echocardiography combined with CT: a case in a juvenile patient
Abstract An anomalous origin of the pulmonary artery (AOPA) from the ascending aorta is a relatively rare but important cardiac malformation that frequently involves the right pulmonary artery (RPA). Its clinical manifestations depend mainly on the associated significant pulmonary hypertension, with...
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| Format: | Article |
| Language: | English |
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BMC
2025-02-01
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| Series: | Journal of Cardiothoracic Surgery |
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| Online Access: | https://doi.org/10.1186/s13019-024-03297-3 |
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| author | Yan-ling Li Ping Xie Jia Wei Zhao-xia Guo |
| author_facet | Yan-ling Li Ping Xie Jia Wei Zhao-xia Guo |
| author_sort | Yan-ling Li |
| collection | DOAJ |
| description | Abstract An anomalous origin of the pulmonary artery (AOPA) from the ascending aorta is a relatively rare but important cardiac malformation that frequently involves the right pulmonary artery (RPA). Its clinical manifestations depend mainly on the associated significant pulmonary hypertension, with an extremely high mortality rate in the first year of life. Here, we present a rare survival case of an 11-year-old child with the disease, who was hospitalized due to intermittent abdominal pain, but without any apparent signs of chest tightness or shortness of breath. The low oxygen saturation as discovered during the physical examination. Subsequent examination with transthoracic echocardiography (TTE) and pulmonary artery computed tomography angiography (CTA) revealed this unexpected congenital malformation. Although the estimated mean pulmonary artery pressure (MAP) from the TTE was 51 mmHg, which seemed to contraindicate corrective cardiac surgery, the limitations of TTE were considered. Consequently, after multidisciplinary consultation, surgical intervention was ultimately decided upon, resulting in a favorable prognosis for the patient. This case provides a new insight for clinicians in the diagnosis and treatment of complex congenital heart diseases. |
| format | Article |
| id | doaj-art-3da432cb225a44a2821cb2dd5d354bac |
| institution | Kabale University |
| issn | 1749-8090 |
| language | English |
| publishDate | 2025-02-01 |
| publisher | BMC |
| record_format | Article |
| series | Journal of Cardiothoracic Surgery |
| spelling | doaj-art-3da432cb225a44a2821cb2dd5d354bac2025-02-09T12:53:50ZengBMCJournal of Cardiothoracic Surgery1749-80902025-02-012011510.1186/s13019-024-03297-3Anomalous origin of a right pulmonary artery identified with echocardiography combined with CT: a case in a juvenile patientYan-ling Li0Ping Xie1Jia Wei2Zhao-xia Guo3School of Traditional Chinese and Western Medicine, Gansu University of Chinese MedicineSchool of Traditional Chinese and Western Medicine, Gansu University of Chinese MedicineDepartment of Cardiology, Gansu Provincial HospitalDepartment of Cardiology, Gansu Provincial HospitalAbstract An anomalous origin of the pulmonary artery (AOPA) from the ascending aorta is a relatively rare but important cardiac malformation that frequently involves the right pulmonary artery (RPA). Its clinical manifestations depend mainly on the associated significant pulmonary hypertension, with an extremely high mortality rate in the first year of life. Here, we present a rare survival case of an 11-year-old child with the disease, who was hospitalized due to intermittent abdominal pain, but without any apparent signs of chest tightness or shortness of breath. The low oxygen saturation as discovered during the physical examination. Subsequent examination with transthoracic echocardiography (TTE) and pulmonary artery computed tomography angiography (CTA) revealed this unexpected congenital malformation. Although the estimated mean pulmonary artery pressure (MAP) from the TTE was 51 mmHg, which seemed to contraindicate corrective cardiac surgery, the limitations of TTE were considered. Consequently, after multidisciplinary consultation, surgical intervention was ultimately decided upon, resulting in a favorable prognosis for the patient. This case provides a new insight for clinicians in the diagnosis and treatment of complex congenital heart diseases.https://doi.org/10.1186/s13019-024-03297-3Anomalous origin of the pulmonary arteryCongenital heart malformationTransthoracic echocardiography |
| spellingShingle | Yan-ling Li Ping Xie Jia Wei Zhao-xia Guo Anomalous origin of a right pulmonary artery identified with echocardiography combined with CT: a case in a juvenile patient Journal of Cardiothoracic Surgery Anomalous origin of the pulmonary artery Congenital heart malformation Transthoracic echocardiography |
| title | Anomalous origin of a right pulmonary artery identified with echocardiography combined with CT: a case in a juvenile patient |
| title_full | Anomalous origin of a right pulmonary artery identified with echocardiography combined with CT: a case in a juvenile patient |
| title_fullStr | Anomalous origin of a right pulmonary artery identified with echocardiography combined with CT: a case in a juvenile patient |
| title_full_unstemmed | Anomalous origin of a right pulmonary artery identified with echocardiography combined with CT: a case in a juvenile patient |
| title_short | Anomalous origin of a right pulmonary artery identified with echocardiography combined with CT: a case in a juvenile patient |
| title_sort | anomalous origin of a right pulmonary artery identified with echocardiography combined with ct a case in a juvenile patient |
| topic | Anomalous origin of the pulmonary artery Congenital heart malformation Transthoracic echocardiography |
| url | https://doi.org/10.1186/s13019-024-03297-3 |
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